Elkiran Ozlem, Karakurt Cemsit, Erdil Nevzat, Disli Olcay Murat, Dagli Adile Ferda
Department of Pediatric Cardiology, Inonu University Faculty of Medicine, Malatya, Turkey.
Congenit Heart Dis. 2013 Nov-Dec;8(6):E174-7. doi: 10.1111/chd.12026. Epub 2012 Dec 27.
Inflammatory myofibroblastic tumor is an uncommon spindle cell tumor, occurring mainly in children and young adults. It is an extremely rare cardiac tumor especially patients under 1 year. Although it is benign, the tumor may be very aggressive locally. The diagnosis of this unusual pediatric cardiac tumor without pathologic specimens is difficult. We report a rare case of inflammatory myofibroblastic tumors of the right ventricle in a 7-month-old girl presenting with respiratory distress and cyanosis.
炎性肌纤维母细胞瘤是一种罕见的梭形细胞肿瘤，主要发生于儿童和年轻人。它是一种极其罕见的心脏肿瘤，尤其是在1岁以下的患者中。尽管它是良性的，但该肿瘤在局部可能具有很强的侵袭性。在没有病理标本的情况下，诊断这种不常见的小儿心脏肿瘤很困难。我们报告了一例罕见的7个月大女童右心室炎性肌纤维母细胞瘤病例，该患儿表现为呼吸窘迫和发绀。
