Shobi A, Tullu M S, Bhatia S, Agrawal M
Department of Pediatrics, Seth G.S. Medical College and KEM Hospital, Mumbai, Maharashtra, India.
J Postgrad Med. 2012 Oct-Dec;58(4):314-7. doi: 10.4103/0022-3859.105468.
Pulmonary arteriovenous malformations are rare vascular anomalies which rarely present in childhood. We discuss a nine-year-old male child who presented with the classical triad of exertional dyspnea, cyanosis and clubbing since six years of age. Pulmonary arteriovenous malformation was suspected on chest radiography and was later confirmed on computed tomography scan. A bubble contrast echocardiography showed the presence of an extracardiac shunt. Pulmonary angiography was done to delineate the anatomy of the pulmonary vasculature and to plan embolization. The child has undergone two sittings of transcatheter coil embolization with improvement in oxygenation.
肺动静脉畸形是一种罕见的血管异常,在儿童期很少出现。我们讨论一名9岁男童,自6岁起就出现劳力性呼吸困难、发绀和杵状指这一典型三联征。胸部X线检查怀疑有肺动静脉畸形,后来计算机断层扫描得以确诊。气泡对比超声心动图显示存在心外分流。进行了肺血管造影以描绘肺血管系统的解剖结构并规划栓塞治疗。该患儿已接受了两次经导管线圈栓塞治疗,氧合情况有所改善。