Orthopedic Surgery Department, Hotel-Dieu de France Hospital, Beirut, Lebanon.
Eur Spine J. 2013 May;22 Suppl 3(Suppl 3):S424-8. doi: 10.1007/s00586-012-2570-y. Epub 2013 Jan 12.
Congenital kyphoscoliosis (CKS) results from abnormal vertebral chondrification. Congenital fibrous bands occur in several locations with variable impact on vertebral development. We report a previously unreported case of a female infant with CKS presenting with an L2 hypoplastic vertebra and a costo-vertebral fibrous band extending to the skin in the form of a dimple. We also describe the therapeutic approach, consisting of surgical excision of the fibrous band and postoperative fulltime bracing, with a 7-year follow-up. We recommend a high index of suspicion in any unusual presentation of CKS and insist on case by case management in such cases.
先天性脊柱后凸侧凸(CKS)是由椎体软骨发育异常引起的。先天性纤维带可发生于多个部位,对椎体发育的影响也各不相同。我们报告了一例女性婴儿 CKS 的病例,该患儿 L2 椎体发育不良,肋椎纤维带延伸至皮肤形成凹陷。我们还描述了治疗方法,包括纤维带的手术切除和术后全时支具固定,随访 7 年。我们建议对任何不寻常的 CKS 表现保持高度警惕,并坚持对这种情况进行个体化治疗。