一名成年患者因鞍上颅咽管瘤引发消瘦性间脑综合征——病例报告

Diencephalic syndrome of emaciation in an adult associated with a suprasellar craniopharyngioma--a case report.

作者信息

Sharma R R, Chandy M J, Lad S D

机构信息

Department of Neurosurgery, Khoula Hospital, Mina Al Fahal, Muscat, Sultanate of Oman.

出版信息

Br J Neurosurg. 1990;4(1):77-80. doi: 10.3109/02688699009000687.

DOI:10.3109/02688699009000687

PMID:2334532

Abstract

An unusual association of diencephalic syndrome of emaciation, pituitary insufficiency for 2 years and suprasellar craniopharyngioma is described in a 45-year-old male. The tumour was found to be adherent to the anterior hypothalamic structures. Following partial excision, irradiation and hormonal replacement he regained his appetite, subcutaneous fat and body weight gradually.

摘要

本文描述了一名45岁男性患者，其患有消瘦性间脑综合征、垂体功能不全2年，并伴有鞍上颅咽管瘤，这种情况较为罕见。发现肿瘤与下丘脑前部结构粘连。经过部分切除、放疗及激素替代治疗后，他的食欲逐渐恢复，皮下脂肪和体重也逐渐增加。