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1型强直性肌营养不良患者的肺血栓栓塞症

Pulmonary thromboembolism in a patient with myotonic dystrophy type 1.

作者信息

Cho Joong-Yang, Seo So-Young, Cho Yong-Jin, Hong Keun-Sik, Park Hee Kyung, Lee Ju Hyun, Lee Sung-Soon

机构信息

Department of Neurology Ilsan Paik Hospital, Inje University College of Medicine, South Korea.

出版信息

Ann Indian Acad Neurol. 2012 Oct;15(4):317-9. doi: 10.4103/0972-2327.104347.

DOI:10.4103/0972-2327.104347
PMID:23349604
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3548377/
Abstract

Thromboembolism is a rare complication in patients with myotonic dystrophy. While immobilization of patients with advanced disease predisposes to high risk for venous thromboembolism, hypercoagulability could account for venous thromboembolism in patients without impaired mobilization. We report a patient with myotonic dystrophy type 1 who developed pulmonary thromboembolism unrelated to immobilization.

摘要

血栓栓塞是强直性肌营养不良患者中一种罕见的并发症。虽然晚期疾病患者的活动受限易导致静脉血栓栓塞的高风险,但高凝状态也可能是活动未受限患者发生静脉血栓栓塞的原因。我们报告1例1型强直性肌营养不良患者发生了与活动受限无关的肺血栓栓塞。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b3f4/3548377/ee9c91e94798/AIAN-15-317-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b3f4/3548377/c045e047688a/AIAN-15-317-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b3f4/3548377/ee9c91e94798/AIAN-15-317-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b3f4/3548377/c045e047688a/AIAN-15-317-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b3f4/3548377/ee9c91e94798/AIAN-15-317-g002.jpg

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引用本文的文献

1
Myotonic dystrophy type 1 and pulmonary embolism: successful thrombus resolution with dabigatran etexilate therapy.1型强直性肌营养不良症与肺栓塞:达比加群酯治疗成功溶解血栓
Acta Myol. 2018 Sep 1;37(3):227-231. eCollection 2018 Sep.

本文引用的文献

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Cardiomyopathy and multiple pulmonary emboli in a patient with myotonic dystrophy.一名患有强直性肌营养不良症的患者出现心肌病和多发性肺栓塞。
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