Cho Joong-Yang, Seo So-Young, Cho Yong-Jin, Hong Keun-Sik, Park Hee Kyung, Lee Ju Hyun, Lee Sung-Soon
Department of Neurology Ilsan Paik Hospital, Inje University College of Medicine, South Korea.
Ann Indian Acad Neurol. 2012 Oct;15(4):317-9. doi: 10.4103/0972-2327.104347.
Thromboembolism is a rare complication in patients with myotonic dystrophy. While immobilization of patients with advanced disease predisposes to high risk for venous thromboembolism, hypercoagulability could account for venous thromboembolism in patients without impaired mobilization. We report a patient with myotonic dystrophy type 1 who developed pulmonary thromboembolism unrelated to immobilization.
血栓栓塞是强直性肌营养不良患者中一种罕见的并发症。虽然晚期疾病患者的活动受限易导致静脉血栓栓塞的高风险,但高凝状态也可能是活动未受限患者发生静脉血栓栓塞的原因。我们报告1例1型强直性肌营养不良患者发生了与活动受限无关的肺血栓栓塞。