Cirstoveanu Catalin, Cinteza Eliza, Marcu Veronica, Bizubac Mihaela, Balomir Alina, Barascu Ileana, Coman Mariana, Balgradean Mihaela
Neonatal Intensive Care Unit, "MS Curie" Emergency Children's Hospital, Bucharest, Romania ; University of Medicine and Pharmacy "Carol Davila", Bucharest, Romania.
Maedica (Bucur). 2012 Jun;7(2):167-72.
We present the case of a newborn with severe pulmonary hypertension, diagnosed with infradiaphragmatic type of total anomalous pulmonary venous connection (TAPVC). The onset was in the first 10 days of life. Diagnosis was made by echocardiography and AngioCT. The pulmonary venous collector was surgically implanted into the left atrium in Germany, but the next month after surgery he developed cardiopulmonary insufficiency and died several days later. We would like to emphasize the importance of prostaglandin E1 administration in this particular case of infradiaphragmatic type of TAPVC and its usefulness in patient's stabilization until surgery. The prognosis in TAPVC, infradiaphragmatic type, is poor and is related mainly to the existence of pulmonary venous obstruction.
我们报告一例患有严重肺动脉高压的新生儿，诊断为膈下型完全性肺静脉异位连接（TAPVC）。发病于出生后的前10天。通过超声心动图和血管CT做出诊断。在德国，肺静脉集合管被手术植入左心房，但术后下个月他出现心肺功能不全，几天后死亡。我们想强调在这种膈下型TAPVC的特殊病例中使用前列腺素E1的重要性及其在手术前稳定患者病情方面的作用。膈下型TAPVC的预后很差，主要与肺静脉梗阻的存在有关。
