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肥厚型心肌病伴中腔梗阻和高左心室内压

Hypertrophic Cardiomyopathy Associated with Mid-cavity Obstruction and High Left Intraventricular Pressure.

作者信息

A Bejiqi Ramush, J Retkoceri Ragip, Sh Bejiqi Hana

机构信息

Department of Cardiology, Pediatrics Clinic, University Clinical Centre of Kosova, Prishtina, Kosova.

出版信息

Acta Inform Med. 2011 Dec;19(4):241-3. doi: 10.5455/aim.2011.19.241-243.

DOI:10.5455/aim.2011.19.241-243
PMID:23407799
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3564173/
Abstract

We report a case of a child, with a rare form of the idiopathic hypertrophic cardiomyopathy, associated with mid-cavity obstruction and high intraventricular peak pressure. Cardiomyopathy, diagnosed antenataly, was followed postnataly and, despite of a lot echocardiographic findings - the growing, development and clinical signs are minimal.

摘要

我们报告了一例患有罕见形式特发性肥厚型心肌病的儿童病例,该病例伴有中腔梗阻和高心室内峰值压力。心肌病在产前被诊断出来,产后进行了随访,尽管有许多超声心动图检查结果,但生长、发育和临床体征均不明显。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/276e/3564173/cbc10edc5241/AIM-19-241_F2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/276e/3564173/37eaad74ac5b/AIM-19-241_F1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/276e/3564173/cbc10edc5241/AIM-19-241_F2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/276e/3564173/37eaad74ac5b/AIM-19-241_F1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/276e/3564173/cbc10edc5241/AIM-19-241_F2.jpg

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Hypertrophic Cardiomyopathy Associated with Mid-cavity Obstruction and High Left Intraventricular Pressure.肥厚型心肌病伴中腔梗阻和高左心室内压
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本文引用的文献

1
The genetics of hypertrophic cardiomyopathy: Teare redux.肥厚型心肌病的遗传学:重温蒂尔研究
Heart. 2008 Oct;94(10):1264-8. doi: 10.1136/hrt.2008.154104. Epub 2008 Jul 24.
2
Echocardiography-guided ethanol septal reduction for hypertrophic obstructive cardiomyopathy.超声心动图引导下乙醇间隔消融术治疗肥厚型梗阻性心肌病
Circulation. 1998 Oct 27;98(17):1750-5. doi: 10.1161/01.cir.98.17.1750.
3
Distribution of left ventricular hypertrophy in hypertrophic cardiomyopathy: a two-dimensional echocardiographic study.肥厚型心肌病中左心室肥厚的分布:一项二维超声心动图研究
J Am Coll Cardiol. 1983 Sep;2(3):437-44. doi: 10.1016/s0735-1097(83)80269-1.
4
Relation between marked changes in left ventricular outflow tract gradient and disease progression in hypertrophic cardiomyopathy.肥厚型心肌病患者左心室流出道梯度显著变化与疾病进展的关系。
Am J Cardiol. 1984 Apr 1;53(8):1103-9. doi: 10.1016/0002-9149(84)90645-3.
5
The mechanism of the intraventricular pressure gradient in idiopathic hypertrophic subaortic stenosis.特发性肥厚性主动脉瓣下狭窄时心室内压力梯度的机制。
Circulation. 1966 Oct;34(4):558-78. doi: 10.1161/01.cir.34.4.558.
6
Apical hypertrophic cardiomyopathy: clinical follow-up and diagnostic correlates.心尖肥厚型心肌病:临床随访与诊断关联
J Am Coll Cardiol. 1990 Jan;15(1):83-90. doi: 10.1016/0735-1097(90)90180-w.
7
Relation between extent of left ventricular hypertrophy and occurrence of sudden cardiac death in hypertrophic cardiomyopathy.肥厚型心肌病患者左心室肥厚程度与心源性猝死发生之间的关系。
J Am Coll Cardiol. 1990 Jun;15(7):1521-6. doi: 10.1016/0735-1097(90)92820-r.