Paediatr Respir Rev. 2013 May;14 Suppl 1:19-21. doi: 10.1016/j.prrv.2013.02.003. Epub 2013 Feb 28.
Non-invasive ventilation is used in patients with cystic fibrosis to treat respiratory failure, as a bridge to transplantation and as an adjunct to airway clearance techniques, despite a limited evidence base, particularly amongst the paediatric population. Where early CF lung disease is complicated by tracheobronchomalacia, we believe CPAP has good theoretical reasons for benefit and we describe a case which serves to illustrate these benefits in clinical practice. As time and technology move on we may begin to see more children with cystic fibrosis being treated with respiratory support.
无创通气用于治疗囊性纤维化患者的呼吸衰竭，作为移植的桥梁，并作为气道清除技术的辅助手段，尽管证据基础有限，特别是在儿科人群中。在早期 CF 肺病合并气管支气管软化的情况下，我们认为 CPAP 具有良好的理论获益依据，我们描述了一个病例，说明了 CPAP 在临床实践中的这些获益。随着时间和技术的发展，我们可能会开始看到更多的囊性纤维化儿童接受呼吸支持治疗。
