Department of Gastroenterology, Tokyo Women's Medical University Yachiyo Medical Center, Yachiyo, Japan.
Jpn J Radiol. 2013 Jun;31(6):405-7. doi: 10.1007/s11604-013-0191-y. Epub 2013 Mar 1.
IgG4-related disease is an emerging clinicopathologic entity. Hypophysitis, diffuse thickening of dura, and enlargement of the trigeminal nerve are well-known intracranial involvements of IgG4-related disease. This report of a case of systemic IgG4-related disease is the first to present neuroimaging of apparent supratentorial meningioma-like lesions and thickening and contrast enhancement of the walls of the intracranial internal carotid arteries. It is important to recognize IgG4-related intracranial pseudotumors so that patients do not undergo unnecessary surgical procedures.
IgG4 相关疾病是一种新兴的临床病理实体。垂体炎、硬脑膜弥漫性增厚和三叉神经增大是 IgG4 相关疾病的众所周知的颅内受累。本病例报告首次提出全身性 IgG4 相关疾病的神经影像学表现为明显的幕上脑膜瘤样病变以及颅内颈内动脉壁的增厚和对比增强。认识 IgG4 相关的颅内假性肿瘤很重要，这样可以避免患者接受不必要的手术。
