漏斗胸中心肌和心脏瓣膜的状况

[Status of the myocardium and heart valves in funnel chest].

作者信息

Iakovlev V M, Goriachev A N, Nechaeva G I, Konev V P, Viktorova I A, Potapov V V

出版信息

Sov Med. 1990(2):6-9.

Abstract

Examinations of 70 patients with keeled deformation of the chest (KDC) have revealed signs of connective tissue dysplasia in all the examinees, as well as heart rhythm and conduction disorders. Echography has shown ventricular and atrial septal defects, mitral valve prolapse, dilatation of the aortic root, tricuspidal valve prolapse, abnormally located chorda. The development of KDC in the presence of external connective tissue stigmata, involvement of the cardiovascular system, changed dermatoglyphic pattern of the palms and fingers (as evidenced by dermatoglyphic analysis), as well as findings of histologic examinations of the cartilage removed in the course of thoracoplasty may indicate a generalized abnormality of the connective tissue in this patient population and KDC may be regarded as one of its manifestations.

摘要

对70例鸡胸畸形（KDC）患者的检查发现，所有受检者均有结缔组织发育异常的体征，以及心律和传导障碍。超声心动图显示室间隔和房间隔缺损、二尖瓣脱垂、主动脉根部扩张、三尖瓣脱垂、腱索位置异常。在存在外部结缔组织体征的情况下KDC的发生、心血管系统受累、手掌和手指皮纹模式改变（皮纹分析证实），以及胸廓成形术过程中切除的软骨组织学检查结果，可能表明该患者群体存在结缔组织的全身性异常，KDC可被视为其表现之一。