Diaz-Murillo Rebeca, Iglesias-Sanchez Carlos, Zapardiel Ignacio
Gynecologic Oncology Unit, La Paz University Hospital, Paseo de la Castellana 262, 28040 Madrid, Spain.
Ecancermedicalscience. 2013 Apr 9;7:303. doi: 10.3332/ecancer.2013.303. Print 2013.
Sarcomas of the broad ligament are very uncommon. To our knowledge, there are no cases published of undifferentiated round cell sarcoma of the broad ligament. Round cell sarcomas are a rare and very aggressive variant, which due to their sensitivity to chemotherapy, have an acceptable prognosis. We report the case of a 27-year-old woman who presented with a pelvic mass with a 7-cm diameter placed on the right broad ligament. After surgery, she was diagnosed with undifferentiated round cell sarcoma of the broad ligament. The patient received adjuvant chemotherapy and radiotherapy, and after 12 years of follow-up, she still remains asymptomatic. Proper differential diagnoses as well as an appropriate adjuvant therapy after surgical treatment seem to be essential to obtain good oncological outcomes in this rare entity.
阔韧带肉瘤非常罕见。据我们所知，尚无阔韧带未分化圆形细胞肉瘤的病例报道。圆形细胞肉瘤是一种罕见且侵袭性很强的变体，由于其对化疗敏感，预后尚可。我们报告一例27岁女性病例，该患者表现为右侧阔韧带上有一个直径7厘米的盆腔肿块。手术后，她被诊断为阔韧带未分化圆形细胞肉瘤。患者接受了辅助化疗和放疗，经过12年的随访，她仍无症状。对于这种罕见疾病，进行恰当的鉴别诊断以及手术治疗后进行适当的辅助治疗似乎对于获得良好的肿瘤学结局至关重要。
