Aschwanden M, Wegmann W
Institut für Pathologie, Kantons Basel-Landschaft.
Schweiz Med Wochenschr. 1990 Jun 2;120(22):836-9.
In a 40-year-old man who collapsed after sporting activity and died shortly after in spite of surgery, autopsy revealed a small ruptured dissecting aneurysm of the left common iliac artery. At the site of rupture, in the aorta and in multiple visceral arteries extensive mucoid degeneration of the media was found. Additional findings (bone deformities, bullous emphysema of the apices of both lungs, and familial affliction) made it possible to establish the diagnosis of an oligosymptomatic form of Marfan syndrome.
一名40岁男性在体育活动后晕倒，尽管接受了手术仍于不久后死亡，尸检发现左髂总动脉有一个小的破裂夹层动脉瘤。在破裂部位、主动脉和多条内脏动脉中，发现中膜有广泛的黏液样变性。其他发现（骨骼畸形、双肺尖部大疱性肺气肿和家族性疾病）使得能够确诊为马方综合征的无症状型。
