Department of Cardiology, Sri Jayadeva Institute of Cardiovascular Sciences and Research, Bangalore, Karnataka, India.
Indian Pediatr. 2013 May 8;50(5):507-8.
Marfan syndrome rarely presents with peripheral artery and pulmonary artery aneurysms. We are presenting a case of a fifteen-year-old boy who presented to us with progressive lower abdominal pulsatile swelling with bruit in the right inguinal region for one month. He had typical marfanoid habitus, though there was no history of similar illness in family. CT angiogram revealed the presence having giant right common iliac aneurysm along with interlobar pulmonary artery aneurysm. He had spontaneous rupture of aneurysm in right common iliac artery.
马凡综合征很少出现外周动脉和肺动脉瘤。我们报告了一例 15 岁男孩，他因右腹股沟区有一个月的进行性下腹部搏动性肿胀和杂音而就诊。他有典型的马凡样体型，但家族中没有类似疾病的病史。CT 血管造影显示存在巨大的右侧髂总动脉瘤和肺叶间肺动脉瘤。他的右侧髂总动脉瘤自发性破裂。
