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表现为帕金森综合征的横窦-乙状窦硬脑膜动静脉瘘

Transverse-sigmoid sinus dural arteriovenous fistula presenting with parkinsonism.

作者信息

Hattori Tomoji, Takeuchi Taku, Kabeya Ryusuke, Ando Kazuhiko, Tosaki Fujio

机构信息

Department of Neurosurgery, Ichinomiya Municipal Hospital, Ichinomiya, Aichi 491-8558, Japan.

出版信息

Neurol Med Chir (Tokyo). 2013;53(4):224-7. doi: 10.2176/nmc.53.224.

DOI:10.2176/nmc.53.224
PMID:23615412
Abstract

Dural arteriovenous fistula (DAVF) is rarely associated with parkinsonism. A 52-year-old woman presented with a rare case of DAVF manifesting as parkinsonism and subsequently akinetic mutism. She showed dramatic recovery after endovascular treatment. We also review 10 published reports of DAVF presenting with parkinsonism. The clinical features of these cases at presentation was more closely compatible with lower body parkinsonism or vascular parkinsonism rather than Parkinson's disease. Most lesions are located at the transverse-sigmoid sinus (TSS) with venous reflux into the straight sinus with probable venous congestion of the basal ganglia. Most importantly, parkinsonism due to TSS DAVF is reversible if embolization is achieved successfully.

摘要

硬脑膜动静脉瘘(DAVF)很少与帕金森症相关。一名52岁女性患者出现了罕见的以帕金森症并随后发展为运动不能性缄默症为表现的DAVF病例。她在接受血管内治疗后出现了显著恢复。我们还回顾了10篇已发表的关于表现为帕金森症的DAVF的报告。这些病例在发病时的临床特征与下肢帕金森症或血管性帕金森症而非帕金森病更为相符。大多数病变位于横窦-乙状窦(TSS),静脉血回流至直窦,可能导致基底节静脉充血。最重要的是,如果成功进行栓塞,由TSS DAVF引起的帕金森症是可逆的。

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