Washio Ken, Nakamura Atsuko, Fukuda Shunpei, Hashimoto Takashi, Horikawa Tatsuya
Department of Dermatology, Nishi-Kobe Medical Center, Kobe, Kurume University School of Medicine and Kurume University Institute of Cutaneous Cell Biology, Kurume, Japan.
Case Rep Dermatol. 2013 Mar 20;5(1):84-7. doi: 10.1159/000350285. Print 2013 Jan.
Lichen planus pemphigoides (LPP) is a rare clinical variant of bullous pemphigoid (BP). A 35-year-old female patient presented to our hospital complaining of pruritic violaceous-colored plaques or papules on the extremities. Tense vesicles were also seen on the soles. Skin biopsies from the papules and vesicles demonstrated lichen planus and BP, respectively. Direct immunofluorescence demonstrated linear IgG and C3 deposition on the basement membrane zone. Indirect immunofluorescence on 1 M NaCl split skin detected IgG reactivity with the epidermal side. Enzyme-linked immunosorbent assay also detected anti-BP180 antibodies. After treatment with oral prednisolone alone had failed, low-dose cyclosporine A (CyA) was added. The clinical symptoms immediately improved and the titer of the anti-BP180 antibodies decreased. Although there is little information about the treatment of recalcitrant LPP, additional CyA appeared to be beneficial.
扁平苔藓样类天疱疮(LPP)是大疱性类天疱疮(BP)的一种罕见临床变体。一名35岁女性患者因四肢出现瘙痒性紫蓝色斑块或丘疹前来我院就诊。足底也可见紧张性水疱。丘疹和水疱的皮肤活检分别显示为扁平苔藓和BP。直接免疫荧光显示基底膜区有线性IgG和C3沉积。在1M NaCl分离皮肤上进行的间接免疫荧光检测到IgG与表皮侧有反应性。酶联免疫吸附试验也检测到抗BP180抗体。单独口服泼尼松龙治疗失败后,加用低剂量环孢素A(CyA)。临床症状立即改善,抗BP180抗体滴度下降。尽管关于顽固性LPP的治疗信息很少,但额外使用CyA似乎有益。