M R Kursiah
Hospital Sultanah Bahiyah, Ophthalmology Department, Alor Star, 05460 Kedah, Malaysia.
Med J Malaysia. 2013 Apr;68(2):173-4.
This case report is about a rare disease with unusual presentation. Failure to recognise atypical presentation may lead to error in managing the patient and cause disastrous complications. Here we highlight a case of Terrien Marginal Degeneration in both eyes with atypical presentation; namely pseudopterygium. A 22 year old man was referred to our centre for iatrogenic right eye corneal perforation after having an atypical pterygium removed at another hospital. On arrival, his vision was 1/60 in both eyes with bilateral cornea Terrien Marginal Degeneration. His right eye anterior chamber was deep with a conjunctival flap covering the perforation site which was located from the 2.30 - 3.30 clock position nasally with no aqueous leak. However after a day his right eye anterior chamber became flat and there was fast aqueous leak from the perforation site. An emergency C shaped peripheral corneal lamellar keratoplasty was performed to seal the perforation. Post operatively his right eye improved to 6/24.
本病例报告讲述的是一种具有不寻常表现的罕见疾病。未能识别非典型表现可能导致对患者的治疗失误并引发灾难性并发症。在此,我们重点介绍一例双眼特发性周边角膜变性的非典型表现病例,即假性翼状胬肉。一名22岁男性在另一家医院接受非典型翼状胬肉切除术后,因医源性右眼角膜穿孔被转诊至我院。入院时,他双眼视力均为1/60,双眼均有特发性周边角膜变性。他的右眼前房深,穿孔部位有结膜瓣覆盖,穿孔位于鼻侧2点30分至3点30分位置,无房水渗漏。然而,一天后他的右眼前房变浅,穿孔部位有快速房水渗漏。急诊行C形周边角膜板层角膜移植术以封闭穿孔。术后他的右眼视力提高到6/24。