Smith J, Sørensen P G, Pallisgaard G
Odense Sygehus, lungemedicinsk afdeling L.
Ugeskr Laeger. 1990 Jun 18;152(25):1832-3.
Diffuse fibrosing alveolitis (DFA) is a disease with progressive, diffuse fibrosis in the interstitial tissue of the pulmonary parenchyma. As a rule, diffuse fibrosing alveolitis is limited to the lungs alone but it may occur as a partial manifestation of a systemic disease. A case report is presented here where diffuse fibrosing alveolitis was encountered in a patient with primary biliary cirrhosis. The pulmonary symptoms dominated the clinical picture and investigation revealed the autoimmune condition.
弥漫性纤维化肺泡炎(DFA)是一种在肺实质间质组织中呈进行性、弥漫性纤维化的疾病。通常,弥漫性纤维化肺泡炎仅局限于肺部,但也可能作为全身性疾病的部分表现出现。本文报告一例原发性胆汁性肝硬化患者并发弥漫性纤维化肺泡炎的病例。肺部症状在临床表现中占主导,检查发现了自身免疫性疾病。