Department of Dermatology, Royal Victoria Infirmary, Newcastle upon Tyne, UK.
Clin Exp Dermatol. 2013 Jul;38(5):517-9. doi: 10.1111/ced.12064. Epub 2013 May 15.
Although catastrophic vascular complications in vascular Ehlers-Danlos Syndrome (EDS) are well recognized, other complications such as flexion contractures and tendon nodules are rarely reported and poorly characterized. We report a young man with vascular EDS, who developed flexion contractures and tendon nodules, causing considerable disability. Limited management strategies are available for these complications, which have continued to prove a challenge to management.
尽管血管型埃勒斯-当洛斯综合征（EDS）的灾难性血管并发症已得到充分认识，但其他并发症，如屈肌挛缩和肌腱结节，很少被报道，也缺乏特征描述。我们报告了一例血管型 EDS 年轻患者，其出现屈肌挛缩和肌腱结节，导致严重残疾。这些并发症的治疗策略有限，且一直是治疗的挑战。
