Westphal W, Müller E, Zabel P, Schlaak M
Medizinische Klinik, Forschungsinstitut Borstel.
Pneumologie. 1990 Feb;44 Suppl 1:544-5.
In three patients with local circumscribed sclerodermia (duration of the disorder 6 months to 3 years), a latent or manifest pulmonary hypertension of the precapillary type in the presence of otherwise unremarkable lung function, radiological and ergometric data, was observed. The pulmonary involvement in this disease would appear to have a relatively early onset.
在3例局限性硬皮病患者（病程6个月至3年）中，观察到在肺功能、放射学和测力计数据无异常的情况下，存在潜在或明显的毛细血管前型肺动脉高压。这种疾病的肺部受累似乎起病相对较早。
