Department of Paediatric Urology, Great Ormond Street Hospital NHS Foundation Trust, Great Ormond Street, London WC1N 3JH, UK.
J Pediatr Urol. 2013 Dec;9(6 Pt B):1103-7. doi: 10.1016/j.jpurol.2013.03.013. Epub 2013 May 18.
To present the outcome of an online survey of the current practice in feminizing surgery for congenital adrenal hyperplasia (CAH) among the specialists attending the IVth World Congress of the International Society of Hypospadias and Disorders of the Sex Development (ISHID), 2011.
An online survey covered 13 individual questions regarding the management and surgical techniques for 46XX CAH patients. All delegates attending the conference were invited to complete this anonymous survey. The data was analysed by three of the authors.
A total of 162 delegates had registered for the conference and 60% of them were paediatric surgeons or paediatric urologists. 65 delegates completed the online survey. Early surgery, before the age of two years, is preferred by 78% of the surgeons and most of them would include clitoroplasty, vaginoplasty and labioplasty. The most frequent surgical technique used for the clitoroplasty is the partial excision of the corpora cavernosa and the skin flap or "U flap" vaginoplasty. Routine vaginal dilatations after puberty are advocated by 28% of the delegates. More than 75% report good outcomes.
Within the limitations of the methodology of this survey, this study suggests that there is agreement in many aspects related with the surgical treatment for 46XX CAH. Self reported outcomes are satisfactory for most of the respondents.
展示 2011 年第四届国际尿道下裂和性别发育障碍协会（ISHID）世界大会与会专家对先天性肾上腺皮质增生症（CAH）女性化手术现状的在线调查结果。
一项在线调查涵盖了 13 个关于 46XX CAH 患者管理和手术技术的问题，邀请所有与会代表匿名填写这份调查问卷。由三位作者对数据进行分析。
共有 162 名代表注册参加会议，其中 60%为小儿外科医生或小儿泌尿科医生。65 名代表完成了在线调查。78%的外科医生赞成在 2 岁之前进行早期手术，他们中的大多数人会进行阴蒂成形术、阴道成形术和阴唇成形术。阴蒂成形术最常用的手术技术是部分切除海绵体和皮瓣或“U 形”阴道成形术。28%的代表主张青春期后常规进行阴道扩张。超过 75%的人报告手术效果良好。
在本调查方法的局限性内，本研究表明，在与 46XX CAH 手术治疗相关的许多方面存在共识。大多数受访者对自我报告的结果感到满意。
