Shivaram U, Shivaram I, Cash M
Brooklyn VA Medical Center 11209.
Chest. 1990 Aug;98(2):491-2. doi: 10.1378/chest.98.2.491.
Tracheobronchomegaly is a distinct clinical and radiologic entity characterized by marked dilatation of the trachea and bronchi. In this report we describe a Marfanoid patient who developed TBM in his adulthood with rapid deterioration, leading to hypercapnic respiratory failure. This case represents an acquired form of TBM in a patient with Marfanoid features which has not been previously described. Tracheobronchomegaly should be considered as a cause of chronic respiratory failure in a young adult and can be diagnosed easily with chest roentgenogram and CAT scan.
气管支气管巨大症是一种独特的临床和放射学疾病,其特征为气管和支气管显著扩张。在本报告中,我们描述了一名类马凡氏体型患者,他在成年期患上气管支气管巨大症并迅速恶化,导致高碳酸血症性呼吸衰竭。该病例代表了一种具有类马凡氏体型特征患者后天获得性气管支气管巨大症的形式,此前尚未有过描述。气管支气管巨大症应被视为年轻成年人慢性呼吸衰竭的一个病因,通过胸部X线片和计算机断层扫描可轻松诊断。