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家族性肥厚型梗阻性心肌病所致的猝死

Sudden unexpected death due to familial hypertrophic obstructive cardiomyopathy.

作者信息

Fernando R

机构信息

Department of Forensic Medicine, Faculty of Medicine, University of Columbo, Sri Lanka.

出版信息

Forensic Sci Int. 1990 Jul;46(3):285-8. doi: 10.1016/0379-0738(90)90314-o.

DOI:10.1016/0379-0738(90)90314-o
PMID:2376368
Abstract

Hypertrophic cardiomyopathy is a familial condition with a very distinct risk of sudden death in males in certain families. The disease appears to be not uncommon in Sri Lanka. A sudden death in a 26-year-old healthy man is reported: At autopsy the heart was 500 g due mainly to left ventricular hypertrophy, and showed histological changes consistent with cardiomyopathy. Symptomless family members of the deceased were subsequently referred to a cardiologist. Cardiomyopathy was diagnosed in one of them.

摘要

肥厚型心肌病是一种家族性疾病,在某些家族中男性有非常明显的猝死风险。这种疾病在斯里兰卡似乎并不罕见。据报道,一名26岁健康男性突然死亡:尸检时心脏重500克,主要是由于左心室肥厚,并且显示出与心肌病一致的组织学变化。死者无症状的家庭成员随后被转诊给心脏病专家。其中一人被诊断出患有心肌病。

相似文献

1
Sudden unexpected death due to familial hypertrophic obstructive cardiomyopathy.家族性肥厚型梗阻性心肌病所致的猝死
Forensic Sci Int. 1990 Jul;46(3):285-8. doi: 10.1016/0379-0738(90)90314-o.
2
Sudden death in hypertrophic cardiomyopathy with normal left ventricular mass.左心室质量正常的肥厚型心肌病患者的猝死
Br Heart J. 1990 May;63(5):308-10. doi: 10.1136/hrt.63.5.308.
3
[Familial hypertrophic obstructive cardiomyopathy as a cause of sudden death].
Soud Lek. 1986 Aug;31(3):41-8.
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A case of sudden and unexpected death due to idiopathic hypertrophic cardiomyopathy in the elderly.一例老年特发性肥厚型心肌病导致的猝死病例。
Am J Forensic Med Pathol. 1981 Jun;2(2):129-33. doi: 10.1097/00000433-198106000-00007.
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Hypertrophic cardiomyopathy without hypertrophy: two families with myocardial disarray in the absence of increased myocardial mass.无肥厚型肥厚型心肌病:两个心肌排列紊乱但心肌质量未增加的家系。
Br Heart J. 1990 May;63(5):287-90. doi: 10.1136/hrt.63.5.287.
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Relation between extent of left ventricular hypertrophy and occurrence of sudden cardiac death in hypertrophic cardiomyopathy.肥厚型心肌病患者左心室肥厚程度与心源性猝死发生之间的关系。
J Am Coll Cardiol. 1990 Jun;15(7):1521-6. doi: 10.1016/0735-1097(90)92820-r.
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Sudden death in hypertrophic cardiomyopathy: associated accessory atrioventricular pathways.肥厚型心肌病中的猝死:相关的房室旁道
Br Heart J. 1980 Mar;43(3):245-51. doi: 10.1136/hrt.43.3.245.
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[Hypertrophic cardiomyopathy. Arrhythmia in hypertrophic cardiomyopathy].[肥厚型心肌病。肥厚型心肌病中的心律失常]
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Failure of amiodarone to prevent ventricular fibrillation (sudden death) in hypertrophic cardiomyopathy.
Can J Cardiol. 1989 Mar;5(2):77-80.
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Sudden death and hypertrophic cardiomyopathy.猝死与肥厚型心肌病
Lancet. 2001 Jun 16;357(9272):1975-6. doi: 10.1016/S0140-6736(00)05039-X.

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