Ghosal A, Pal R B, Das S K, Das T
N.R.S Medial College & Hospital, Neurology, 138, AJC Bose Road, Kolkata-700014, Kolkata, West Bengal 700014, India.
Med J Malaysia. 2012 Oct;67(5):532-3.
Adult onset still's disease usually presents with high grade intermittent fever, polyarthritis, salmon pink evanescent rash and hepatosplenomegaly. Pulmonary involvement in the form of pneumonitis, as a presenting feature is very rare. We report a case of a young lady who presented with fever, cough and respiratory distress. Chest X-ray revealed patchy infiltration in left upper lung zone. She was subsequently diagnosed as Adult onset Still's disease. There was no improvement in clinical condition despite five days of antibiotics. On trans-bronchial lung biopsy (TBLB) proved she had interstitial pneumonitis and responded dramatically to steroid treatment.
成人斯蒂尔病通常表现为高热、间歇性发热、多关节炎、鲑鱼粉红色的一过性皮疹和肝脾肿大。以肺炎形式出现的肺部受累作为首发特征非常罕见。我们报告一例年轻女性患者,她出现发热、咳嗽和呼吸窘迫。胸部X线显示左上肺野有斑片状浸润。她随后被诊断为成人斯蒂尔病。尽管使用了五天抗生素,临床状况并无改善。经支气管肺活检(TBLB)证实她患有间质性肺炎,对类固醇治疗反应显著。