Akbulut Sami, Yilmaz Mehmet, Kahraman Aysegul, Yilmaz Sezai
Inonu University Faculty of Medicine, Malatya, Turkey.
J Infect Dev Ctries. 2013 Jun 15;7(6):489-93. doi: 10.3855/jidc.2712.
Budd-Chiari syndrome is an uncommon disorder characterized by the thrombotic or non-thrombotic obstruction of hepatic venous outflow anywhere along the venous course from the hepatic venules to the junction of the inferior vena cava and the right atrium. The etiology of Budd-Chiari syndrome is classified as primary, attributable to intrinsic intraluminal thrombosis or the development of venous webs; or secondary, caused by intraluminal invasion by a parasite or malignant tumor or extraluminal compression by an abscess, solid tumor, or cyst, such as a hydatid cyst. In this study, we present a case of a giant hydatid cyst manifesting Budd-Chiari syndrome symptoms and signs by compressing the inferior vena cava and hepatic veins. In brief, the case demonstrates that hydatid disease should be considered in the differential diagnosis of Budd-Chiari Syndrome in areas such as Turkey, where hydatid disease is endemic.
布加综合征是一种罕见的疾病,其特征是从肝小静脉到下腔静脉与右心房交界处的静脉行程中任何部位出现肝静脉流出道的血栓形成或非血栓形成性梗阻。布加综合征的病因分为原发性,归因于管腔内固有血栓形成或静脉网的形成;或继发性,由寄生虫或恶性肿瘤的管腔内侵犯或脓肿、实体瘤或囊肿(如包虫囊肿)的管腔外压迫引起。在本研究中,我们报告了一例巨大包虫囊肿通过压迫下腔静脉和肝静脉而表现出布加综合征症状和体征的病例。简而言之,该病例表明,在包虫病流行的地区,如土耳其,在布加综合征的鉴别诊断中应考虑包虫病。