Hypertension Center, Department of Cardiology, Fuwai Hospital, Peking Union Medical College and Chinese Academy of Medical Sciences, Beijing, China.
Clin Cardiol. 2013 Aug;36(8):E7-10. doi: 10.1002/clc.22149. Epub 2013 Jun 18.
Fibromuscular dysplasia (FMD) is a nonatherosclerotic, noninflammatory arterial disease, commonly involving the renal arteries. Here we report a case of a 16-year-old Chinese male who was found to have severe hypertension with proteinuria for 2 years. Computed tomography showed absence of the left kidney and enlargement of the right kidney. Subsequent angiography confirmed the above findings and revealed narrowing of both the upper and lower branches of the right renal artery caused by FMD. These combined lesions are very rare, and individuals affected are at increased risk of renal dysfunction if left untreated. Treatment with percutaneous balloon angioplasty is the first choice in such a patient and usually results in optimal outcomes.
纤维肌性发育不良（FMD）是一种非动脉粥样硬化、非炎症性的动脉疾病，常累及肾动脉。在此我们报告一例 16 岁的中国男性，发现其患有严重高血压伴蛋白尿 2 年。计算机断层扫描显示左肾缺失，右肾增大。随后的血管造影证实了上述发现，并显示由 FMD 引起的右肾上下分支狭窄。这些联合病变非常罕见，如果不治疗，受影响的个体患肾功能障碍的风险增加。经皮球囊血管成形术是此类患者的首选治疗方法，通常可获得最佳效果。
