Department of Radiology, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave., MLC 5031, Cincinnati, OH, 45229-3026, USA,
Pediatr Radiol. 2013 Dec;43(12):1656-61. doi: 10.1007/s00247-013-2737-7. Epub 2013 Jul 7.
Pyloric atresia is an uncommon congenital gastric outlet obstruction, accounting for only 1% of gastrointestinal atresias. Up to 55% of cases have associated anomalies, the most common of which is epidermolysis bullosa. Fetal MRI findings of the epidermolysis bullosa-pyloric atresia association have not been previously reported. We present a case of this association diagnosed by prenatal MRI with corroborative postnatal imaging and surgical findings.
幽门闭锁是一种罕见的先天性胃出口梗阻，仅占胃肠道闭锁的 1%。多达 55%的病例伴有相关畸形，最常见的是大疱性表皮松解症。大疱性表皮松解症-幽门闭锁的胎儿 MRI 表现以前尚未报道过。我们报告了一例通过产前 MRI 诊断的该种关联，同时提供了产后影像学和手术发现来佐证。
