Department of Anesthesiology and Pain Medicine, Yonsei University College of Medicine, Seoul, Korea.
Korean J Pain. 2013 Jul;26(3):299-302. doi: 10.3344/kjp.2013.26.3.299. Epub 2013 Jul 1.
Erythromelalgia is a rare neurovascular pain syndrome characterized by a triad of redness, increased temperature, and burning pain primarily in the extremities. Erythromelalgia can present as a primary or secondary form, and secondary erythromelalgia associated with a myeloproliferative disease such as essential thrombocythemia often responds dramatically to aspirin therapy, as in the present case. Herein, we describe a typical case of a 48-year-old woman with secondary erythromelalgia linked to essential thrombocythemia in the unilateral hand. As this case demonstrates, detecting and visualizing the hyperthermal area through infrared thermography of an erythromelalgic patient can assist in diagnosing the patient, assessing the therapeutic results, and understanding the disease course of erythromelalgia.
红斑性肢痛症是一种罕见的神经血管性疼痛综合征,其特征为三联征:主要发生在四肢的发红、温度升高和灼烧样疼痛。红斑性肢痛症可表现为原发性或继发性,与骨髓增生性疾病(如特发性血小板增多症)相关的继发性红斑性肢痛症常对阿司匹林治疗有显著反应,本病例即如此。在此,我们描述了一例 48 岁女性单侧手部继发于特发性血小板增多症的红斑性肢痛症的典型病例。正如本病例所示,通过对红斑性肢痛症患者进行红外热成像检测和可视化其高温区域,有助于诊断患者、评估治疗效果以及了解红斑性肢痛症的病程。