囊性纤维化中的假性巴特综合征。
Pseudo-Bartter's syndrome in cystic fibrosis.
作者信息
Kennedy J D, Dinwiddie R, Daman-Willems C, Dillon M J, Matthew D J
机构信息
Respiratory Unit, Hospital for Sick Children, London.
出版信息
Arch Dis Child. 1990 Jul;65(7):786-7. doi: 10.1136/adc.65.7.786.
Abstract
Seven cases of cystic fibrosis complicated by chronic salt depletion and failure to thrive were studied. After replacement of the salt deficit, the metabolic abnormalities resolved, and weight gain was rapid. This should be considered as a differential diagnosis in children who have been diagnosed as having cystic fibrosis, but who fail to thrive despite standard treatment.
摘要
对7例囊性纤维化合并慢性盐耗竭和生长发育不良的病例进行了研究。补充盐分缺乏后，代谢异常得到解决，体重迅速增加。对于已被诊断为囊性纤维化，但尽管接受了标准治疗仍生长发育不良的儿童，应将此视为一种鉴别诊断。
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本文引用的文献
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Studies in the physiology of sweating in cystic fibrosis. II. Elevated night sweating rates.囊性纤维化患者出汗生理的研究。II. 夜间出汗率升高
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