Sivkova S N, Bogdanov E I, Zaĭkova F M, Morozova E A, Aiupova V A, Zabbarova A T, Shaĭmardanova R M
Zh Nevrol Psikhiatr Im S S Korsakova. 2013;113(6):11-6.
Fever-induced refractory epileptic encephalopathy of school-age children is a rare epileptic syndrome that causes difficulties in diagnosis at the initial stage of disease. It is characterized by sudden onset with multifocal refractory status epilepticus in previously healthy children with normal development. Later, children suffer from resistant focal epilepsy in the combination with cognitive deficit and behavioral difficulties. Authors describe a clinical case of fever-induced refractory epileptic encephalopathy of school-age children in a child of 7 years old. Aspects of etiology, pathogenesis, clinical manifestation, differential diagnosis, treatment and prognosis of the disease are discussed.
学龄儿童发热性难治性癫痫性脑病是一种罕见的癫痫综合征，在疾病初期诊断困难。其特征为先前发育正常的健康儿童突然起病，伴有多灶性难治性癫痫持续状态。随后，儿童会出现耐药性局灶性癫痫，并伴有认知缺陷和行为障碍。作者描述了一名7岁儿童患学龄儿童发热性难治性癫痫性脑病的临床病例。并讨论了该疾病的病因、发病机制、临床表现、鉴别诊断、治疗及预后等方面。
