Department of Cardiology, Hangzhou First People's Hospital, Hangzhou 310006, China.
J Zhejiang Univ Sci B. 2013 Aug;14(8):759-62. doi: 10.1631/jzus.BQICC710.
Marfan syndrome is a systemic connective tissue disease that could affect the cardiovascular system and eventually lead to heart enlargement and heart failure with high mortality, mainly due to progressive heart failure and/or sudden cardiac death caused by malignant arrhythmia. Here we report that a patient received a cardiac resynchronization therapy-defibrillator (CRT-D) with a pre-monitor function for heart failure and experienced obvious improvements in his cardiac function. Postoperative follow-up showed that the patient had reduced morbidity and hospitalization for heart failure, and also experienced improved quality of life.
马凡综合征是一种系统性结缔组织疾病,可累及心血管系统,最终导致心脏扩大和心力衰竭,病死率高,主要是由于进行性心力衰竭和/或恶性心律失常导致的心脏性猝死。本研究报道了 1 例马凡综合征患者因心力衰竭行心脏再同步治疗除颤器(CRT-D)植入,并带有心力衰竭预监测功能,患者心功能明显改善。术后随访发现患者心力衰竭的发病率和住院率降低,生活质量得到提高。