Helen Onakpoya Oluwatoyin, Ajite K O, Oyelami O A, Asaleye C M, Adeoye A O
Department of Surgery, College of Health Sciences, Obafemi Awolowo University, Ile-Ife, Nigeria.
Niger Med J. 2013 May;54(3):200-2. doi: 10.4103/0300-1652.114571.
Bone infarction involving the orbit in sickle cell disease is not common. Bilateral orbital infarction in a previously undiagnosed sickle cell hemoglobinopathy has not been previously reported. In this report, we present a case of an 11-year-old previously undiagnosed sickle cell disease Nigerian girl with severe acute bilateral orbital infarction and retinal detachment to highlight that hemoglobinopathy induced orbital infarction should be considered in African children with acute onset proptosis with or without previous history of sickle cell hemoglobinopathy.
镰状细胞病累及眼眶的骨梗死并不常见。此前未曾报道过在先前未诊断出的镰状细胞血红蛋白病患者中发生双侧眼眶梗死的情况。在本报告中,我们呈现了一例11岁先前未诊断出镰状细胞病的尼日利亚女孩,她患有严重的急性双侧眼眶梗死和视网膜脱离,以强调对于有急性突眼发作且有无镰状细胞血红蛋白病既往史的非洲儿童,应考虑血红蛋白病诱发的眼眶梗死。