Ann Thorac Surg. 2013 Aug;96(2):675-7. doi: 10.1016/j.athoracsur.2012.12.007.
We report the case of a 42-year-old man who presented with kyphosis resulting from a giant symptomatic costal osteochondroma around the left fourth rib. The osteochondroma on the left side of the back was 56 cm × 47 cm × 33 cm and was painful. The size and growth of the tumor suggested a malignant transformation of a large costal osteochondroma. Multiple osteochondromas were also found on the legs. The patient's family history revealed hereditary characteristics. This patient was clinically diagnosed as a case of multiple familial osteochondromatosis. Complete removal of the tumor relieved the symptoms, and histopathologic examination confirmed malignant transformation of chondrosarcoma. There was no recurrence after 16 months of follow-up.
我们报告了一例 42 岁男性患者，因左侧第四肋骨周围巨大的症状性肋软骨瘤导致后凸畸形。背部左侧的肋软骨瘤大小为 56cm×47cm×33cm，有疼痛感。肿瘤的大小和生长提示大型肋软骨瘤发生恶性转化。腿部也发现了多个骨软骨瘤。患者家族史显示出遗传性特征。该患者临床诊断为多发性家族性骨软骨瘤病。肿瘤完全切除后缓解了症状，组织病理学检查证实为软骨肉瘤恶变。随访 16 个月后无复发。
