Cedars Ari, Joseph Susan, Ludbrook Philip
, 660 S. Euclid Ave, Campus Box 8086, Saint Louis, MO, 63110, USA,
Curr Treat Options Cardiovasc Med. 2013 Oct;15(5):587-601. doi: 10.1007/s11936-013-0257-2.
Fontan type palliations are a group of operations employed in patients with only one functional ventricle. These procedures take the normally parallel pulmonary and systemic circulations and place them in series to reestablish separation between the two. The Fontan circulation established by such operations is a unique, artificial physiologic entity. Although the Fontan circulation supports patients for decades, patients eventually experience progressive heart failure. As this growing group of patients reaches adulthood, there is a need for general cardiologists as well as adult congenital heart disease specialists to be familiar with the long-term sequelae of the Fontan circulation. The purpose of the present review is to summarize the limited available data on heart failure of the Fontan, its natural history, evaluation, and management.
Fontan类姑息手术是用于仅有一个功能心室的患者的一组手术。这些手术将正常并行的肺循环和体循环改为串联，以重新建立两者之间的分隔。通过此类手术建立的Fontan循环是一种独特的人工生理实体。尽管Fontan循环能维持患者数十年，但患者最终会出现进行性心力衰竭。随着这一不断壮大的患者群体步入成年，普通心脏病专家以及成人先天性心脏病专科医生都需要熟悉Fontan循环的长期后遗症。本综述的目的是总结关于Fontan循环心力衰竭的有限现有数据、其自然病史、评估及管理。
