Yamada Kazunori, Tsumaru Shinichi, Mochizuki Shingo, Mochizuki Takaaki
Department of Cardiovascular Surgery, Tsuchiya General Hospital, Hiroshima, Japan.
Kyobu Geka. 2013 Aug;66(9):837-40.
We encountered a case of total anomalous pulmonary venous connection with a drainage vein following an unusual course. The drainage vein, after emerging from the right lung, crossed the midline and drained into the innominate vein. Along the course of this vein, severe stenosis was present in the region wedged between the aortic arch and pulmonary artery, leading to severe pulmonary congestion. The common pulmonary vein was well developed. There was no other intracardiac malformation except atrial septal defect. No heterotaxy syndrome associated. Because echocardiography was unable to provide a complete picture of the pulmonary veins and drainage veins, multidetector-row computed tomography was performed to ascertain the anatomy. Emergency surgical intervention was carried out and anastomosis of the common pulmonary vein to the left atrium was performed. The postoperative course was favorable.
我们遇到了一例完全性肺静脉异位连接病例，其引流静脉走行异常。引流静脉自右肺发出后，越过中线，汇入无名静脉。在该静脉走行过程中，位于主动脉弓和肺动脉之间的区域存在严重狭窄，导致严重的肺淤血。共同肺静脉发育良好。除房间隔缺损外，无其他心内畸形。未合并内脏反位综合征。由于超声心动图无法完整显示肺静脉和引流静脉，遂行多排螺旋计算机断层扫描以明确解剖结构。实施了急诊手术干预，将共同肺静脉与左心房进行吻合。术后病程顺利。
