Düzgün Nurşen, Küçükşahin Orhan, Atasoy Kayhan Çetin, Togay Işıkay Canan, Gerede Demet Menekşe, Erden Ayşe, Sahap Seda Kaynak, Ibiş Muhammed Arif, Ateş Aşkın
Department of Internal Medicine-Rheumatology, Ankara University, Faculty of Medicine, Akademik Yerleşke, Sıhhıye, 06100 Ankara, Turkey.
Case Rep Rheumatol. 2013;2013:637015. doi: 10.1155/2013/637015. Epub 2013 Jul 2.
We present three patients with Behçet's disease associated with intracardiac thrombus and pulmonary vascular involvement. One of these patients had also Budd-Chiari syndrome. All patients were treated with corticosteroid plus monthly intravenous cyclophosphamide as first line treatment and with no recurrences. Immunosuppressive therapy was successful in the treatment of intracardiac thrombus and also in the regression of pulmonary vascular thromboses in these patients. Intracardiac thrombus in Behçet's disease is rarely seen. Behçet's disease should be remembered in the differential diagnosis of the patients with intracardiac mass, especially in patients from the Mediterranean and Middle East populations.
我们报告了3例患有白塞病且伴有心内血栓形成和肺血管受累的患者。其中1例患者还患有布加综合征。所有患者均接受皮质类固醇加每月静脉注射环磷酰胺作为一线治疗,且无复发。免疫抑制疗法成功治疗了这些患者的心内血栓,也使肺血管血栓消退。白塞病中的心内血栓很少见。在鉴别诊断心内肿块患者时,尤其是来自地中海和中东地区人群的患者,应考虑白塞病。