Brandt Erik, Pilt Anette Pedersen, Bisgaard Thue
Kirurgisk Afdeling, Køge Sygehus, 4600 Køge.
Ugeskr Laeger. 2013 Aug 26;175(35):1963-4.
Primary intra-abdominal undifferentiated high-grade pleomorphic sarcoma is rare with only 40 cases described worldwide. We describe a case of a patient who presented with mechanical bowel obstruction with abdominal undifferentiated high-grade pleomorphic sarcoma. Five-year survival rates have been reported as low as 40-55%, especially due to late diagnosis. Rare diagnoses as in our patient emphasize the need for close collaboration between pathologists, radiologists and surgeons.
原发性腹腔内未分化高级别多形性肉瘤很罕见,全球仅报道过40例。我们描述了1例因腹部未分化高级别多形性肉瘤出现机械性肠梗阻的患者。据报道,其5年生存率低至40% - 55%,尤其是由于诊断较晚。像我们患者这样的罕见诊断凸显了病理学家、放射科医生和外科医生密切协作的必要性。