Division of Pulmonary and Critical Care Medicine, Stanford University, Stanford, California, USA ; Vera Moulton Wall Center for Pulmonary Vascular Disease, Stanford University, Stanford, California, USA.
Pulm Circ. 2013 Apr;3(2):436-9. doi: 10.4103/2045-8932.114780.
Chronic constrictive pericarditis (CP) is a relatively rare condition in which the pericardium becomes fibrotic and noncompliant, eventually resulting in heart failure due to impaired ventricular filling. The only curative treatment is pericardiectomy. Classically, CP does not usually cause severe pulmonary hypertension. When attempting to differentiate CP from restrictive cardiomyopathy, the presence of severely elevated pulmonary arterial pressure is used as a diagnostic criterion ruling against CP. We present a case of proven recurrent pericardial constriction following pericardiectomy presenting with severe pulmonary hypertension.
慢性缩窄性心包炎(CP)是一种相对罕见的疾病,心包变得纤维化和顺应性降低,最终导致心力衰竭,原因是心室充盈受损。唯一的根治性治疗方法是心包切除术。经典情况下,CP 通常不会导致严重的肺动脉高压。在试图将 CP 与限制型心肌病区分开来时,严重升高的肺动脉压被用作排除 CP 的诊断标准。我们报告了一例经证实的心包切除术后复发性心包缩窄的病例,该患者表现为严重的肺动脉高压。