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鼻前庭横纹肌样间叶性错构瘤

Rhabdomyomatous mesenchymal hamartoma of nasal vestibule.

作者信息

Kang Ju Wan, Park Heae Surng, Kim Jeong Hong

机构信息

From the *Department of Otorhinolaryngology, Yongin Severance Hospital, Yonsei University College of Medicine, Yongin; †Department of Pathology, Gangnam Severance Hospital, Yonsei University College of Medicine, Seoul; and ‡Department of Otorhinolaryngology, Jeju National University School of Medicine, Jeju, Korea.

出版信息

J Craniofac Surg. 2013;24(5):e481-3. doi: 10.1097/SCS.0b013e3182903357.

DOI:10.1097/SCS.0b013e3182903357
PMID:24036822
Abstract

Rhabdomyomatous mesenchymal hamartoma is a rare congenital tumor and usually occurring in the head and neck. Characteristically, this tumor is composed of various mesenchymal elements such as adipose tissue, blood vessels, collagen fibers, elastic fibers, and peripheral nerves in random orientation. We present a 7-year-old boy with an intranasal mass developed after the trauma and who had a diagnosis of rhabdomyomatous mesenchymal hamartoma.

摘要

横纹肌样间叶性错构瘤是一种罕见的先天性肿瘤,通常发生于头颈部。其特征是,该肿瘤由多种间叶成分组成,如脂肪组织、血管、胶原纤维、弹性纤维和随机排列的周围神经。我们报告一例7岁男孩,其在创伤后鼻腔内出现肿物,诊断为横纹肌样间叶性错构瘤。

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Arch Craniofac Surg. 2017 Dec;18(4):292-295. doi: 10.7181/acfs.2017.18.4.292. Epub 2017 Dec 23.