Zargari Omid, Asadi Masih, Azimi Seyyede Zeinab, Mesbah Alireza
Skin Research Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
York University, Toronto, Canada.
J Cutan Pathol. 2021 Sep;48(9):1182-1184. doi: 10.1111/cup.14044. Epub 2021 Jun 4.
Rhabdomyomatous mesenchymal hamartoma (RMH) is a rare congenital malformation of the dermis and subcutaneous tissue. Usually, RMH occurs in the midline of the face and neck region. We described a case of RMH presenting as telangiectasia in a 57-year-old man with a history of pityriasis lichenoides chronicus. Histopathological examination revealed a subepidermal haphazard proliferation of striated muscular tissue perpendicular to the epidermis. These bundles of striated muscular tissue were admixed with adnexal structures. The diagnosis was consistent with RMH. RMH is more common in the neonatal period or in young children, but we should consider it as part of a differential diagnosis in older adults as well.
横纹肌瘤样间叶性错构瘤（RMH）是一种罕见的真皮和皮下组织先天性畸形。通常，RMH发生于面颈部中线部位。我们报道了一例57岁男性患者，有慢性苔藓样糠疹病史，其RMH表现为毛细血管扩张。组织病理学检查显示表皮下有垂直于表皮的横纹肌组织杂乱增生。这些横纹肌组织束与附属器结构混合存在。诊断符合RMH。RMH在新生儿期或幼儿中更为常见，但在老年人中我们也应将其视为鉴别诊断的一部分。
