Gowda Narayana, Kumar Mohan J, Kumar Ajith K
Dr. Narayana Gowda BS, Orthopaedics, PES Medical College, Kuppam, Chitore 517425,, Andra Pradesh, India,
Ann Saudi Med. 2013 Jul-Aug;33(4):368-71. doi: 10.5144/0256-4947.2013.368.
Ochronic arthropathy of hip (Black Hip) is a rare clinical manifestation of congenital disorder of amino acid metabolism characterized by a classic triad: (1) degenerative arthritis, (2) ochronotic pigmentation, and (3) urine that turns black on long standing or alkalinization. We report a case of ochronic arthropathy of the left hip joint that was successfully treated by total hip arthroplasty.
This is a case study conducted at PES Medical College, Andhra Pradesh, India.
A 60-year-old female patient came with a history of progressive pain in her left hip joint for the last 8 months. She was diagnosed to be suffering from ochronic arthritis of left hip.
After tissue confirmation she was operated with total hip replacement. At the end of 2 years, the patient was symptom free without any implant loosening.
Ochronotic arthropathy is a rare metabolic disorder that can be underdiagnosed many a times. Early management is only symptomatic, and advanced cases need surgical intervention. Vitamin preparations are given because of the influence of vitamin C on tyrosine and phenylalanine metabolism. In the cases of severe degenerative arthritis of hip, total hip replacement may be considered as a surgical option.
髋部褐黄病性关节病（黑髋）是一种罕见的氨基酸代谢先天性疾病的临床表现，其特征为典型的三联征：（1）退行性关节炎，（2）褐黄病色素沉着，（3）尿液长期放置或碱化后变黑。我们报告一例成功通过全髋关节置换术治疗的左髋关节褐黄病性关节病病例。
这是一项在印度安得拉邦PES医学院开展的病例研究。
一名60岁女性患者，有过去8个月左髋关节进行性疼痛病史。她被诊断为左髋褐黄病性关节炎。
经组织确诊后，她接受了全髋关节置换手术。2年后，患者无症状，植入物无松动。
褐黄病性关节病是一种罕见的代谢紊乱疾病，很多时候可能会漏诊。早期治疗仅为对症治疗，晚期病例需要手术干预。由于维生素C对酪氨酸和苯丙氨酸代谢有影响，所以给予维生素制剂。对于严重的髋部退行性关节炎病例，全髋关节置换可作为一种手术选择。
