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鼻腔持续气道正压通气(CPAP)治疗哈利曼-施特雷夫综合征阻塞性睡眠呼吸暂停

Nasal continuous positive airway pressure (CPAP) therapy for obstructive sleep apnea in Hallermann-Streiff syndrome.

作者信息

Ryan C F, Lowe A A, Fleetham J A

机构信息

Department of Medicine, University of British Columbia, Vancouver, Canada.

出版信息

Clin Pediatr (Phila). 1990 Feb;29(2):122-4. doi: 10.1177/000992289002900212.

DOI:10.1177/000992289002900212
PMID:2406080
Abstract

An 8-year-old girl with Hallermann-Streiff syndrome (oculomandibulofacial syndrome) was examined. She had a history of severe snoring, reported nocturnal apnea, excessive daytime hypersomnolence, nocturnal enuresis, and failure to thrive. Overnight polysomnography confirmed severe obstructive sleep apnea. Long-term nasal continuous positive airway pressure (CPAP) therapy completely relieved the obstructive sleep apnea and was associated with improved weight gain and growth.

摘要

对一名患有哈勒曼-施特雷夫综合征(眼下颌面综合征)的8岁女孩进行了检查。她有严重打鼾史,报告有夜间呼吸暂停、白天过度嗜睡、夜间遗尿以及生长发育迟缓。夜间多导睡眠图证实存在严重阻塞性睡眠呼吸暂停。长期鼻持续气道正压通气(CPAP)治疗完全缓解了阻塞性睡眠呼吸暂停,并与体重增加和生长改善相关。

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Nasal continuous positive airway pressure (CPAP) therapy for obstructive sleep apnea in Hallermann-Streiff syndrome.鼻腔持续气道正压通气(CPAP)治疗哈利曼-施特雷夫综合征阻塞性睡眠呼吸暂停
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