Department of Thoracic Surgery, Süleyman Demirel University, Medical Faculty, Isparta, Turkey.
Department of Thoracic Surgery, Süleyman Demirel University, Medical Faculty, Isparta, Turkey.
Ann Thorac Surg. 2013 Oct;96(4):1461-1464. doi: 10.1016/j.athoracsur.2013.01.082.
Inflammatory myofibroblastic tumor (IMT) is a rare benign neoplasm. It is a challenging disease because the symptoms and radiologic findings are diverse and nonspecific. Although pulmonary IMT is the most common form, pleural origin is an extremely rare clinical entity. Nuchal fibroma (NF) is another rare benign neoplasm. We report herein a case of pleural IMT with concomitant NF in a 15-year-old girl. To the best of our knowledge, this is the first report suggesting an association between IMT and NF, and our case had the largest reported intrathoracic IMT. Moreover, we found a possible association between IMT and increased CA-125 levels.
炎性肌纤维母细胞瘤（IMT）是一种罕见的良性肿瘤。它是一种具有挑战性的疾病，因为其症状和影像学表现多种多样且无特异性。尽管肺 IMT 是最常见的形式，但胸膜起源是一种极为罕见的临床实体。神经纤维瘤（NF）是另一种罕见的良性肿瘤。我们在此报告一例 15 岁女孩同时患有胸膜 IMT 和 NF。据我们所知，这是首例提示 IMT 和 NF 之间存在关联的病例，且我们的病例中胸腔内 IMT 是报道中最大的。此外，我们发现 IMT 与 CA-125 水平升高之间可能存在关联。
