肋骨纤维结构不良中的肉瘤样变性。

Sarcomatous degeneration in fibrous dysplasia of the rib cage.

机构信息

Department of Thoracic and Vascular Surgery, Antwerp University Hospital, Edegem, Belgium.

Department of Pathology, Antwerp University Hospital, Edegem, Belgium.

出版信息

Ann Thorac Surg. 2013 Oct;96(4):e89-e90. doi: 10.1016/j.athoracsur.2013.04.131.

DOI:10.1016/j.athoracsur.2013.04.131

PMID:24088499

Abstract

Malignant degeneration in fibrous dysplasia is a rare occurrence. Most cases are reported in polyostotic fibrous dysplasia with predisposition of the femur, tibia, maxilla, and mandible. The most commonly observed malignant tumors are osteosarcoma, fibrosarcoma, and chondrosarcoma. We describe a case of a low-grade osteosarcoma occurring in polyostotic fibrous dysplasia of the rib cage in a 50-year-old man.

摘要

纤维结构不良的恶性变是一种罕见的情况。大多数病例发生在多骨纤维结构不良中，且易发生于股骨、胫骨、上颌骨和下颌骨。最常见的恶性肿瘤是骨肉瘤、纤维肉瘤和软骨肉瘤。我们描述了一例 50 岁男性发生于肋骨多骨纤维结构不良的低度恶性骨肉瘤。