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播散性瘢痕结节病可能预示结节病患者出现肺部受累。

Disseminated scar sarcoidosis may predict pulmonary involvement in sarcoidosis.

作者信息

Su Ozlem, Onsun Nahide, Topukçu Buğçe, Ozçelik Hatice Kutbay, Cakıter Alkım Unal, Büyükpınarbaşılı Nur

机构信息

Bezmialem Vakif University, Medical Faculty, Department of Dermatovenereology, Adnan Menderes Bulvarı, Vatan Caddesi, Fatih, Istanbul, Turkey, 34093. Bezmialem Vakif University, Medical Faculty, Department of Chest Diseases, Adnan Menderes Bulvarı, Vatan Caddesi, Fatih, Istanbul, Turkey, 34093. Bezmialem Vakif University, Medical Faculty, Department of Pathology, Adnan Menderes Bulvarı, Vatan Caddesi, Fatih, Istanbul, Turkey, 34093. Corresponding author:

出版信息

Acta Dermatovenerol Alp Pannonica Adriat. 2013 Sep;22(3):71-4.

Abstract

Sarcoidosis is a chronic, inflammatory, multi-organ disease of unknown origin that is characterized by non-caseating granuloma formation in affected organs. Cutaneous involvement is reported in 25% of patients with sarcoidosis. Scar sarcoidosis is rare but is clinically specific for skin sarcoidosis. Systemic involvement is seen in most patients with scar sarcoidosis. We present a case of scar sarcoidosis in a 30-year-old male that developed infiltrated nodules on old scars, including on his penile shaft, which is rare, and that also had pulmonary involvement. Scar sarcoidosis should be considered in the differential diagnosis of changes in all scar areas and should be investigated for systemic involvement.

摘要

结节病是一种病因不明的慢性炎症性多器官疾病,其特征是在受影响的器官中形成非干酪样肉芽肿。据报道,25%的结节病患者有皮肤受累。瘢痕结节病罕见,但在皮肤结节病中具有临床特异性。大多数瘢痕结节病患者有全身受累。我们报告一例30岁男性的瘢痕结节病,该患者在包括阴茎干在内的旧瘢痕上出现浸润性结节,这种情况罕见,且该患者也有肺部受累。在所有瘢痕区域变化的鉴别诊断中应考虑瘢痕结节病,并应检查是否有全身受累。

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