Department of Neurosurgery, Poursina Hospital, Guilan University of Medical Sciences, Rasht,
Arch Iran Med. 2013 Oct;16(10):606-7.
Primary intracranial leiomyosarcomas are rare tumors that arise from the mesenchymal cells of the dura mater or cerebral blood vessels Here we report the case of an extra axial leiomyosarcoma in the right parieto-occipital region of a 19-year-old male who had normal clinical and laboratory findings. Diagnostic imaging showed bony destruction, dural involvement and no parenchymal invasion. No primary site was found after metastasis work up. Specific serology tests were negative. The patient underwent a craniotomy, total tumor resection, duraplasty and skull reconstruction. He received radiotherapy and after 18 months of follow-up, no clinical and radiological signs of recurrence have been found.
颅内原发性平滑肌肉瘤较为罕见，来源于硬脑膜或脑血管的间叶细胞。我们在此报告一例 19 岁男性患者右顶枕部的颅外轴索平滑肌肉瘤，患者临床及实验室检查均正常。影像学检查显示骨质破坏、硬脑膜受累，无实质侵犯。转移灶检查未发现原发病灶。特殊的血清学检查均为阴性。患者接受了开颅手术、全肿瘤切除术、硬脑膜修补和颅骨重建。术后接受了放疗，随访 18 个月后，未发现临床和影像学复发迹象。
