Allevi F, Rabbiosi D, Colletti G, Felisati G, Rezzonico A, Ronchi P, Biglioli F
Department of Cranio-Maxillo-Facial Surgery San Paolo Hospitalniversity of Milan, Milan, Italy:2 Department of Otolaryngology, San Paolo Hospital, University of Milan, Milan, Italy:3 Department of Cranio-Maxillo-Facial Surgery Sant' Anna Hospital, Como, Italy -
Minerva Stomatol. 2013 Oct;62(10):387-95.
Rhabdomyomas are rare mesenchymal benign tumors of striated muscle origin that can be classified into cardiac and extracardiac types. Cardiac rhabdomyomas are considered as hamartomatous lesion because of their association with phacomatosis. Extracardiac type is further classified into adult, fetal and genital form, depending on the individual tumor's degree of differentiation. Adult head and neck rhabdomyomas are rare pathologies of adult patients, with a male predominance. The occurrence of multifocality is a rare manifestation of this uncommon lesion. Presenting symptoms are related to the location and dimension of the tumors and they include upper airway obstruction, Eustachian tube dysfunction, dysphagia and mucosal and neck mass. Because of their high rate of recurrence, radical resection is the treatment of choice of this kind of tumors. In this article is reported a rare and particularly large case of head and neck adult rhabdomyoma, presenting with an history of sleep apnea and night-time stridor.
横纹肌瘤是一种罕见的起源于横纹肌的间叶性良性肿瘤,可分为心脏型和心脏外类型。心脏横纹肌瘤因其与错构瘤病相关,被视为错构瘤性病变。心脏外类型根据肿瘤的分化程度进一步分为成人型、胎儿型和生殖器型。成人头颈部横纹肌瘤是成人患者罕见的病理情况,男性居多。多灶性的出现是这种罕见病变的一种少见表现。临床表现与肿瘤的位置和大小有关,包括上呼吸道梗阻、咽鼓管功能障碍、吞咽困难以及黏膜和颈部肿块。由于其高复发率,根治性切除是这类肿瘤的首选治疗方法。本文报道了一例罕见的、特别大的成人头颈部横纹肌瘤病例,该患者有睡眠呼吸暂停和夜间喘鸣病史。