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一种罕见耳鼻喉肿瘤的突发临床病程:多发性骨髓瘤继发髓外浆细胞瘤的临床症状

Sudden clinical course of an unusual ENT tumour: clinical pictures of extramedullary plasmacytoma secondary to multiple myeloma.

作者信息

Pagella F, Canzi P, Matti E, Benazzo M

机构信息

Department of Otorhinolaryngology, University of Pavia, IRCCS Policlinico "S. Matteo" Foundation, Pavia, Italy.

出版信息

Acta Otorhinolaryngol Ital. 2013 Oct;33(5):347-9.

Abstract

Extramedullary plasmacytoma (EMP) is a rare monoclonal plasmacytic proliferation involving upper airways in 80% of cases. The heterogeneous pattern of frequency in the head and neck area may result in insidious clinical expressions that are potentially lethal for the patient. The presentation and management of two suggestive clinical photographs characterized by sudden and aggressive EMP development secondary to multiple myeloma are discussed.

摘要

髓外浆细胞瘤(EMP)是一种罕见的单克隆浆细胞增殖性疾病,80%的病例累及上呼吸道。头颈部区域频率的异质性模式可能导致隐匿的临床症状,对患者具有潜在致命性。本文讨论了两张具有提示性的临床照片,其特征为继发于多发性骨髓瘤的突然且侵袭性的EMP发展情况及处理。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/04ae/3825039/cd12a0500bc7/0392-100X-33-347-g001.jpg

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