Kalenahalli Kiran V, Garg Navneet, Goolahally Lakshmikantha N, Reddy Somasekhara P, Iyengar Jayanth
Department of Radiology and Imaging, Sagar Hospitals, Bangalore, Karnataka, India.
J Clin Neonatol. 2013 Jul;2(3):146-8. doi: 10.4103/2249-4847.120009.
Pulmonary sequestration is a rare malformation, wherein a portion of lung is non-functional and is not in normal continuity with the tracheo-bronchial tree, and may derive its blood supply from systemic vessels. Two types are described: Intralobar and extralobar types. Intralobar sequestration is more common type, which shares visceral pleura of the involved lobe and is localized within the normal pulmonary parenchyma. Whereas extralobar forms are uncommon and are totally separate from the lung and usually have own covering. Infra-diaphragmatic pulmonary sequestration is of extralobar type and is extremely rare, and usually is associated with other congenital malformations. We present an extremely rare case of isolated infra-diaphragmatic pulmonary sequestration which was antenatally detected and followed up with postnatal CT scan, where it masqueraded as suprarenal mass, and was surgically treated. This case emphasises to add a differential diagnosis of malformation in congenital supra-renal masses, which remain stable in size and appearance, and hence avoid immediate surgery.
肺隔离症是一种罕见的畸形，其中一部分肺组织无功能，与气管支气管树无正常连续性，且其血液供应可能来自体循环血管。可分为两种类型：叶内型和叶外型。叶内型肺隔离症较为常见，与受累肺叶的脏层胸膜相连，位于正常肺实质内。而叶外型较少见，与肺完全分离，通常有自己的被膜。膈下肺隔离症属于叶外型，极为罕见，通常与其他先天性畸形相关。我们报告了一例极其罕见的孤立性膈下肺隔离症病例，该病例在产前被检测到，并在出生后进行CT扫描随访，其在CT上表现为肾上腺肿块，最终接受了手术治疗。该病例强调在先天性肾上腺肿块的鉴别诊断中应增加对畸形的考虑，这类肿块在大小和外观上保持稳定，因此应避免立即手术。
