Uncini A, Treviso M, Basciani M, Gambi D
Electroencephalogr Clin Neurophysiol. 1987 Feb;66(2):132-6. doi: 10.1016/0013-4694(87)90182-9.
Three patients with autosomal dominant Strümpell's familial spastic paraplegia (SFSP) were evaluated by means of somatosensory evoked potentials (SEPs) from upper and lower limb and determination of sural nerve conduction velocity. Findings of normal sural nerve conduction but reduced amplitude and poor definition of SEPs with normal latencies on peroneal nerve stimulation support a pattern of central nervous system degeneration characterized by a selective involvement of centrally directed axons within the gracile fasciculi.
对3例常染色体显性遗传性施特吕姆佩尔家族性痉挛性截瘫（SFSP）患者进行了评估，采用了上下肢体感诱发电位（SEP）以及腓肠神经传导速度测定。腓肠神经传导正常，但在腓总神经刺激时SEP波幅降低且波形清晰度差、潜伏期正常，这些结果支持一种以薄束内中枢传导轴突选择性受累为特征的中枢神经系统变性模式。
