Sato Hisashi, Yoshikai Masaru, Miho Takahiro, Nakanishi Harumi, Irie Koji
Department of Cardiovascular Surgery, Shin-Koga Hospital, Kurume, Japan.
Kyobu Geka. 2013 Dec;66(13):1183-5.
We herein report a very rare case of a primary left atrial myxofibrosarcoma. A 61-year-old female presented with dyspnea and a wet cough. Chest X-ray film showed cardiomegaly and pulmonary congestion. Echocardiography and computed tomography revealed a left atrial tumor obstructing blood flow to the left ventricle. She was diagnosed with acute congestive heart failure due to functional mitralstenosis secondary to a left atrial tumor, and an emergency operation was performed. The tumor, which occupied left atrium, attached to the posterior wall of the left atrium and to the mitral valve, but had not invaded the left atrial wall. The tumor was removed from the left atrial wall, preserving the mitral valve and valve leaflets. The patient's post operative course was uneventful. The pathological diagnosis was myxofibrosarcoma, which rarely develops in the heart.
我们在此报告一例非常罕见的原发性左房黏液纤维肉瘤病例。一名61岁女性出现呼吸困难和湿性咳嗽。胸部X线片显示心脏扩大和肺充血。超声心动图和计算机断层扫描显示左房肿瘤阻碍血液流向左心室。她被诊断为因左房肿瘤继发功能性二尖瓣狭窄导致的急性充血性心力衰竭，并接受了急诊手术。该肿瘤占据左房，附着于左房后壁和二尖瓣，但未侵犯左房壁。肿瘤从左房壁切除，保留二尖瓣和瓣叶。患者术后恢复顺利。病理诊断为黏液纤维肉瘤，这在心脏中很少发生。
